Glucosidase Alpha, Acid (GaA)

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LYAG; Acid Alpha-Glucosidase; Lysosomal Alpha-Glucosidase; Pompe Disease Glycogen Storage Disease Type II; Acid Maltase; Aglucosidase Alfa

Glucosidase Alpha, Acid (GaA)

Lysosomal alpha-glucosidase is an enzyme that is encoded by the GAA gene. Error's in this gene cause glycogen storage disease type II (Pompe disease).

This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.

Organism species: Homo sapiens (Human)

CATALOG NO.PRODUCT NAMEAPPLICATIONS
ProteinsRPA177Hu01Recombinant Glucosidase Alpha, Acid (GaA)Positive Control; Immunogen; SDS-PAGE; WB.
RPA177Hu02Recombinant Glucosidase Alpha, Acid (GaA)Positive Control; Immunogen; SDS-PAGE; WB.
AntibodiesPAA177Hu01Polyclonal Antibody to Glucosidase Alpha, Acid (GaA)WB; IHC; ICC; IP.
MAA177Hu22Monoclonal Antibody to Glucosidase Alpha, Acid (GaA)WB; IHC; ICC; IP.
PAA177Hu02Polyclonal Antibody to Glucosidase Alpha, Acid (GaA)WB; IHC; ICC; IP.
Assay KitsSEA177HuELISA Kit for Glucosidase Alpha, Acid (GaA)Enzyme-linked immunosorbent assay for Antigen Detection.

Organism species: Mus musculus (Mouse)

CATALOG NO.PRODUCT NAMEAPPLICATIONS
ProteinsRPA177Mu01Recombinant Glucosidase Alpha, Acid (GaA)Positive Control; Immunogen; SDS-PAGE; WB.
RPA177Mu02Recombinant Glucosidase Alpha, Acid (GaA)Positive Control; Immunogen; SDS-PAGE; WB.
AntibodiesPAA177Mu01Polyclonal Antibody to Glucosidase Alpha, Acid (GaA)WB; IHC; ICC; IP.
PAA177Mu02Polyclonal Antibody to Glucosidase Alpha, Acid (GaA)WB; IHC; ICC; IP.
Assay KitsSEA177MuELISA Kit for Glucosidase Alpha, Acid (GaA)Enzyme-linked immunosorbent assay for Antigen Detection.

Organism species: Rattus norvegicus (Rat)

CATALOG NO.PRODUCT NAMEAPPLICATIONS
ProteinsRPA177Ra01Recombinant Glucosidase Alpha, Acid (GaA)Positive Control; Immunogen; SDS-PAGE; WB.
RPA177Ra02Recombinant Glucosidase Alpha, Acid (GaA)Positive Control; Immunogen; SDS-PAGE; WB.
AntibodiesPAA177Ra01Polyclonal Antibody to Glucosidase Alpha, Acid (GaA)WB; IHC; ICC; IP.
PAA177Ra02Polyclonal Antibody to Glucosidase Alpha, Acid (GaA)WB; IHC; ICC; IP.
Assay KitsSEA177RaELISA Kit for Glucosidase Alpha, Acid (GaA)Enzyme-linked immunosorbent assay for Antigen Detection.
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